Laugier-Hunziker syndrome: an important differential diagnosis for Peutz-Jeghers syndrome.

نویسندگان

  • A K Lampe
  • P J Hampton
  • K Woodford-Richens
  • I Tomlinson
  • C M Lawrence
  • F S Douglas
چکیده

Laugier-Hunziker syndrome (LHS) is a rare sporadic disorder, which shares some dermatological features with Peutz-Jeghers syndrome (PJS). However, whereas PJS is associated with hamartomatous gastrointestinal polyposis and carries a high risk of malignancy justifying intensive screening protocols, LHS is known to be an entirely benign disease with no systemic manifestations, which requires patient reassurance as the only intervention.

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عنوان ژورنال:
  • Journal of medical genetics

دوره 40 6  شماره 

صفحات  -

تاریخ انتشار 2003