Laugier-Hunziker syndrome: an important differential diagnosis for Peutz-Jeghers syndrome.
نویسندگان
چکیده
Laugier-Hunziker syndrome (LHS) is a rare sporadic disorder, which shares some dermatological features with Peutz-Jeghers syndrome (PJS). However, whereas PJS is associated with hamartomatous gastrointestinal polyposis and carries a high risk of malignancy justifying intensive screening protocols, LHS is known to be an entirely benign disease with no systemic manifestations, which requires patient reassurance as the only intervention.
منابع مشابه
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عنوان ژورنال:
- Journal of medical genetics
دوره 40 6 شماره
صفحات -
تاریخ انتشار 2003